DOI: http://dx.doi.org/10.18203/issn.2454-2156.IntJSciRep20221053

Prosthodontic rehabilitation of a pediatric patient with hypohidrotic ectodermal dysplasia: a case report

Pinki Gupta, Ankita Singh, Himanshi Yadav

Abstract


The aim of this case report was to prosthodontically rehabilitate and boost the psychological development of the patient. Ectodermal dysplasia is a hereditary condition presented with abnormal development of tissues of ectodermal origin such as hair, skin, nails, and teeth. This condition generally presented with following signs and symptoms; dental abnormalities, onychodysplasia, hypohidrosis, and hypotrichosis. Ectodermal dysplasia usually has an X-linked recessive trait, with most common being of hypohidrotic ectodermal dysplasia also known as Christ-Siemens-Touraine syndrome. This case report describes the prosthetic rehabilitation with conventional dentures in maxillary arch and tooth supported overdenture in mandibular arch of a young boy with hypohidrodic ectodermal dysplasia. Prosthetic treatment is very helpful to these patients from functional, psychological, and psychosocial points of view. Need for continued dental treatment is necessary.


Keywords


Hypohidrotic ectodermal dysplasia, Christ-Siemens-Touraine syndrome, Prosthetic rehabilitation, Multidisciplinary management, Pediatric patient

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